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Table 2 Disease activity and damage: IMACS core set measurements

From: Assessment of patients with idiopathic inflammatory myopathies and isolated creatin-kinase elevation

Disease activity

 Physician global activity—VAS/Likert

 Patient/parent global activity—VAS/Likert

 Muscle strength—manual muscle test (MMT)

 Physical function—[C]HAQ, CMAS

 Laboratory—muscle enzymes

 Extra-muscular activity—MDAAT

Damage

 Myositis Damage Index (MDI)

 Physician global damage—VAS/Likert

 Physical function—[C]HAQ

  1. C childhood, CMAS Childhood Myositis Assessment Scale, VAS visual analog scale, HAQ health assessment questionnaire, MDAAT myositis disease activity assessment tool, IMACS International Myositis Assessment and Clinical Studies Group