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Table 2 The combinations of different autoimmune diseases present in our patient (in italics), with other possible diseases present in a patient with APS/MAS-3

From: A rare combination of type 3 autoimmune polyendocrine syndrome (APS-3) or multiple autoimmune syndrome (MAS-3)

Autoimmune thyroid diseases: Graves’ disease, Hashimoto’s thyroiditis, endocrine ophthalmopathy, pretibial myxoedema

Type 1 DM (LADA)

Chronic atrophic gastritis

Autoimmune leukopenia

Sjögren’s syndrome

Ulcerative colitis

Anti-phospholipid syndrome

Hirata’s syndrome

Pernicious anemia

Vitiligo

Systemic lupus erythematodes

Premature ovarian failure

Celiac disease

Alopecia

Discoid lupus erythematodes

Adeno-hypophysitis

Other inflammatory bowel diseases

Bullous Skin diseases

Rheumatoid arthritis

Neuro-hypophysitis

Primary biliary cirrhosis

Chronic idiopathic urticaria

Mixed connective tissue disease

Chronic hypoparathyroidism

Autoimmune hepatitis

Myasthenia gravis

Seronegative arthritis

 

Sclerosing cholangitis

Stiff-person syndrome

Systemic sclerosis

 

Autoimmune pancreatitis

Multiple sclerosis

Dermato/polymyositis

  

Autoimmune anemia

Vasculitis

  

Autoimmune thrombocytopenia

 

Endocrine glands

Gastrointestinal tract and liver

Skin

Autoimmune rheumatic disorders

Muscles

Vasculitis

Nervous system

 

Haematologic system

 

3A

3B

3C

3D

  1. APS/MAS-3 autoimmune polyendocrine syndrome/multiple autoimmune syndrome type 3