Table 1 Diagnostic criteria for IP

Major criteria

 Erythema followed by blisters/vesicles

 Skin involvement stage I (first weeks of life to age four months)

 Hyperpigmented streaks and whorls that respects Blaschko’s lines

 Skin involvement stage III (age four months to 16 years)

 Pale, hairless, atrophic linear streaks or patches

 Skin involvement stage IV (adolescence through adulthood)

Minor criteria

 Hypodontia, anodontia, microdontia, and abnormally shaped teeth

 Alopecia

 Mild ridging or pitting of the nails, Onychogryphosis

 Peripheral neovascularization of the retina