| SSc (n = 44) |
---|---|
F (%) vs M (%) | 42 (95.4Â %) vs 2 (4.6Â %) |
Median age, yy(range) | 66 (34–80) |
Median disease duration, yy (range) | 9 (1–16) |
D (%) vs L (%) | 10 (22.7Â %) vs 34 (77.3Â %) |
anti-Scl70 (+) (%) | 12 (27.3Â %) |
ACA (+) (%) | 22 (50Â %) |
Others Abs (%)a | 10 (22.7Â %) |
Iloprost (%) | 25 (56.8Â %) |
Bosentan (%) | 7 (15.9Â %) |
Ulcers (%) | 15 (34.1Â %) |
Early NVC pattern (%) | 6 (13.6Â %) |
Active NVC pattern (%) | 20 (45.4Â %) |
Late NVC pattern (%) | 18 (40.9Â %) |
GE disease (%) | 36 (81.8Â %) |
sPAP >45Â mmHg (%) | 3 (6.8Â %) |
DLCO <50Â % (%) DLCO/AV <50Â % (%) | 7 (15.9Â %) 1 (2.3Â %) |
FVC <80Â % (%) | 8 (18.2Â %) |
Honeycombing lung (%) | 4 (9.1Â %) |
Rodnan skin score >14 (%) | 9 (20.4Â %) |