Table 1 Clinical features frequent in 112 Italian patients
Clinical manifestations | N/total (%) | Diffuse 47 (41.9) N/diff (%) | Limited 65 (58) N/lim (%) | p |
|---|---|---|---|---|
Gastrointestinal involvement (esophagus) | 71 (63) | 29 (62) | 42 (65) | ns |
Lung fibrosis | 73 (65) | 40 (85) | 33 (50.7) | <0.01 |
Pulmonary hypertension | 44 (39) | 23 (49) | 21 (32) | 0.08(ns) |
Renal involvementa | 4 (3.6) | 4 (8.5) | – | – |
Myositis | 4 (3.6) | 4 (8.5) | – | – |
Multi-organ involvement | 59 (52) | 31 (65.9) | 28 (43) | <0.01 |
Renal crisis | 2 (1.7) | 2 (4.2) | – | – |
Deceased | 4 (3) | 2 (4.2) | 2 (3) | – |